Open AccessAmelogenesis Imperfecta – Case Series and Management
Author(s) -
Rishi Tyagi Prof,
Namita Kalra Prof Hod,
Amit Khatri Asso Prof,
Harsh Vijay Singh,
Mayank Sharma,
Puja Sabherwal
Publication year - 2019
Publication title -
clinical dentistry
Language(s) - English
Resource type - Journals
eISSN - 0974-4916
pISSN - 0974-3979
DOI - 10.33882/clinicaldent.13.24697
Subject(s) - amelogenesis imperfecta , enamel paint , osteogenesis imperfecta , dentition , permanent dentition , dentistry , inheritance (genetic algorithm) , dentinogenesis imperfecta , orthodontics , medicine , psychology , genetics , anatomy , biology , gene
Amelogenesis imperfecta (AI) incorporates an assemblage of hereditary diseases that involve the defective formation or calcication of enamel. Also known by varied names such as Hereditary enamel dysplasia, Hereditary brown enamel, Hereditary brown opalescent teeth, this defect is entirely ectodermal, since mesodermal components are unaffected. AI is typically characterized by generalized enamel defects in both primary and permanent dentition. The AI trait can be transmitted by either autosomal dominant, autosomal recessive, or X-linked modes of inheritance.AI has a marked impact on aesthetics, function and psychology of the patient. Early intervention and dental rehabilitation should be carried out with strong emphasis on the preventive care and strict follow up schedule.Key words: Amelogenesis imperfecta, developmental anomaly, Dental Rehabilitation