Open AccessPulmonary Alveolar Microlithiasis(PAM)
Author(s) -
Devendra Nath Sarkar,
Ismail Hossain,
Mahmudul Haque,
Akm Zahin,
Shahin Miah,
MA Ohab,
Altaf Hossain,
Beauty Saha
Publication year - 2016
Publication title -
medicine today
Language(s) - English
Resource type - Journals
eISSN - 2408-8714
pISSN - 1810-1828
DOI - 10.3329/medtoday.v27i2.30044
Subject(s) - medicine , chest radiograph , asymptomatic , pulmonary function testing , chest pain , radiology , lung , disease , rare disease , interstitial lung disease , respiratory failure , radiography
PAM is a rare parenchymal Lung disease. Very few case report are available about PAM in Bangladesh. It is diagnosed incidentally during chest radiograph. It is a autosomal recessive disease and is associated with sporadic or familial mutation of SLC 34A2 gene. Many patients are asymptomatic and have either normal or restrictive pulmonary function. Some patients remain static and others progress into pulmonary dysfunction, respiratory failure and corpulmonale. The disease is usually discovered up to 40 years and there is no definitive treatment of this disease. Chest radiograph, HRCT used lung biopsy (transbronchial or open) are the main investigations. This patient come with chest pain and dyspnoea on exertion and nonproductive cough and diagnosed as PAM incidentally during chest radiograph. On the basis of clinical features and laboratory finding, we diagnosed him a case of PAM a very rare condition. As there is no definitive treatment, we treat himsymptomatically.Medicine Today 2015 Vol.27(2): 40-43