Open AccessPoland Syndrome- A Rare Congenital Condition
Author(s) -
Homayra Tahseen Hossain,
Abul Kashem Khandaker,
Quazi Tarikul Islam,
Ham Nazmul Ahasan,
Munshi Mb Md Shoaib Adnan,
Najmul Islam
Publication year - 2018
Publication title -
journal of bangladesh college of physicians and surgeons/journal of bangladesh college of physicians and surgeons
Language(s) - English
Resource type - Journals
eISSN - 2309-6365
pISSN - 1015-0870
DOI - 10.3329/jbcps.v36i4.38186
Subject(s) - medicine , poland syndrome , etiology , bronchiectasis , pediatrics , surgery , lung
Named after Sir Alfred Poland, Poland syndrome is a rare congenital anomaly classically characterized by the absence of unilateral chest wall muscles and sometimes ipsilateral symbrachydactyly (abnormally short and webbed fingers). The aetiology is probably a vascular disruption sequence of the subclavian arteries. In most cases, Poland Syndrome is sporadic. We report a 26 year old male patient with typical features of Poland Syndrome associated with bronchiectasis and mitral valve prolapse- a very rare association. To the best of our knowledge, this is the first documented case of a Poland Syndrome with rare association reported from Bangladesh.J Bangladesh Coll Phys Surg 2018; 36(4): 166-169