Open AccessEctopia Cordis: A Rare Congenital Heart Disease
Author(s) -
Naharuma Aive Hyder Chowdhury,
Mohammad Sharifuzzaman,
Mohammad Abul Kalam Azad,
Tuhin Haque,
Jesmin Hossain
Publication year - 2019
Publication title -
cardiovascular journal
Language(s) - English
Resource type - Journals
eISSN - 2309-6357
pISSN - 2071-0917
DOI - 10.3329/cardio.v11i2.40419
Subject(s) - medicine , intracardiac injection , pulmonary artery banding , heart disease , mediastinum , great vessels , pulmonary artery , cardiology , ventricle , great arteries , surgery , radiology
Three days old female presented with beating heart outside the thoracic cavity. This is a rare congenital abnormality associated multiple abnormalities. Patient came with features of infection. To diagnose routine blood investigation along with echocardiography and CT angiogram of heart,great vessel and abdomen were done. She was diagnosed as functionally single ventricle with hypoplastic branch pulmonary artery with malposed great artery with anomalous pulmonary venous drainage. Thisis lethal variety of ectopic cordis. Our patient had no adequate space in mediastinum to replace heart and she was in septicemia, so managed medically. Patient expired at her 6thday due to sepsis and intracardiac complex congenital heart disease.
Cardiovasc. j. 2019; 11(2): 183-186