Open AccessSinus Histocytosis with Splenomegaly in Children- A Rare Case Report
Author(s) -
Kuntal Roy,
Fabia Hannan Mone,
Syed Khairul Amin,
Ekhlasur Rahman,
Soma Halder
Publication year - 2019
Publication title -
anwer khan modern medical college journal
Language(s) - English
Resource type - Journals
eISSN - 2304-5701
pISSN - 2221-836X
DOI - 10.3329/akmmcj.v10i2.44132
Subject(s) - medicine , histiocyte , lymph , rosai–dorfman disease , sinus (botany) , cervical lymphadenopathy , histiocytosis , lung , sinus histiocytosis with massive lymphadenopathy , disease , pathology , dermatology , botany , biology , genus
Sinus Histiocytosis/Rosai-Dorfman Disease (RDD) are benign, rare proliferative disorder caused by over production and accumulation of specific type of white blood cell (Phagocytic Histiocyte) in the lymph nodes of the body. Here, lymphadenopathy mostly painless and commonly found in the neck (cervical) but may occur in other areas of the body such as skin, lung, central nervous system, kidney (less than 5%). Predominantly it affects the young age group of children, adolescents or young adults. In spite of spontaneous remissions, treatment strategies can be different according to involvement and severity (RDD- Seldom life threatening disease).
Anwer Khan Modern Medical College Journal Vol. 10, No. 2: July 2019, P 176-178