Open AccessNtenga Syndrome: About an Observation
Author(s) -
Patrice Ntenga,
Kantenga Dieu Merci Kabulo,
H Mbayo,
Christene Bora,
Kamadore Touré,
Dophra Ngoy Nkulu
Publication year - 2020
Publication title -
advances in neurology and neuroscience
Language(s) - English
Resource type - Journals
ISSN - 2690-909X
DOI - 10.33140/an.03.03.03
Subject(s) - levetiracetam , medicine , etiology , status epilepticus , pediatrics , hyperostosis , valproic acid , epilepsy , psychiatry , surgery
Ntenga syndrome, is one of the highly epileptogenic, non-metabolic craniopathy whose aetiology is not yet known. This syndrome makes a differential diagnosis with that of Morgagni-Stewart-Morel which is rare and / or rarely mentioned in current clinical practice (entity made of frontal hyperostosis, neuropsychiatric and endocrine disorders). We report here a 58 years old female patient from Lubumbashi/ Democratic republic of Congo, followed for several years for multiform seizures, in whom the explorations of a status epilepticus, made possible to set up a new syndromic entity, called Ntenga syndrome made of a symptomatic triad (persistent multiform epileptic seizures, absence of endocrine disorder, hyperostosis frontalis interna). To date, a therapeutic protocol made of valproic acid and levetiracetam has significantly reduced to one seizure per month or even every 2 months. I think it is not without interest to report a very rare and / or new entity in the clinic.