INTRAOCULAR MALIGNANT TERATOID MEDULLOEPITHELIOMA

Malignant teratoid medulloepithelioma is an uncommon unilateral intraocular tumor,occuring typically in children. This report concerns a 4-year-old boy, who presentedwith loss of vision, pain and proptosis of the left eye and showed mass in betweeneyelids. Histopathologically, the tumor was composed of pseudostratified primitive-appearing epithelium dispersed in cords, strands, tubules & glands, which wereseparated by a cystic spaces, filled with pale eosinophilic material. Foci of glial tissue,cartilage , bone, skeletal muscle and fatty tissue were recognized. In addition, scleralextension of tumor, Homer-Wright like and Flexner-Wintersteiner like rosettes andfoci of necrosis were also present. The differentiation from retinoblastoma wasdiscussed.Key Words: Malignant medulloepithelioma, eyeball, heteroplasia.