Open AccessSubconjunctival Mass as Rare Presentation of Even Rarer Intraocular Medulloepithelioma: A Case Report
Author(s) -
Santosh Chaudhary,
Vinayak Regmi,
Sangeeta Shah,
Purbesh Adhikari
Publication year - 2020
Publication title -
journal of nepal medical association
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.176
H-Index - 19
eISSN - 1815-672X
pISSN - 0028-2715
DOI - 10.31729/jnma.5269
Subject(s) - enucleation , medicine , presentation (obstetrics) , ciliary body , orbit (dynamics) , eye enucleation , surgery , ophthalmology , engineering , aerospace engineering
Medulloepithelioma is a rare childhood embryonal tumor arising from the non-pigmented ciliary epithelium of the pars plicata. We report a case of an 11-year-old male who presented with painless loss of vision of the right eye for the last three years and progressively increasing mass on the superior aspect of the globe for the last three months. On ocular examination, a firm, non-tender mass of 4cm x 3cm was noted in the superior aspect of the globe. CT-Scan of the orbit was suggestive of a foreign body with a haemorrhage or infection. The patient underwent enucleation with minimal manipulation. Histopathological examination of the enucleated globe revealed medulloepithelioma. The intraocular medulloepithelioma presentation is often late and masquerading, which may lead to extraocular extension and metastasis and ultimately unfavorable prognosis.