Open AccessProximal epithelioid sarcoma of the vulva: A case report and review of the literature
Author(s) -
Mercedes Bravo-Taxa,
Luis Taxa-Rojas,
Aldo López-Blanco
Publication year - 2021
Publication title -
clinical surgery research communications
Language(s) - English
Resource type - Journals
eISSN - 2573-0096
pISSN - 2573-0088
DOI - 10.31491/csrc.2021.09.081
Subject(s) - vulva , epithelioid sarcoma , medicine , lymphadenectomy , sarcoma , wide local excision , metastasis , incidence (geometry) , surgery , general surgery , cancer , pathology , physics , optics
Primary sarcomas of the vulva are rare, with an incidence of 1.5% to 5% of all vulvar malignancies. There are only 41 cases described in the English literature of proximal epithelioid sarcoma of the vulva, which also constitutes a highly aggressive neoplasm with a high rate of recurrence and metastasis. We are reporting the first case of vulvar epithelioid sarcoma reported in our country, Peru, and Latin America. We present the case of a 53-year-old woman with no significant history who presented a large tumor mass of 25 cm in the left hemivulva of 2 years of evolution, associated with intense pain. She underwent radical surgical resection with left inguinopelvic lymphadenectomy and reconstruction of Rectus Abdominal Muscle Myocutaneous Flaps (TRAM).