Open AccessBilateral Internal Auditory Canal (IAC) Duplication with Congenital Sensorineural Hearing Loss (SNHL)-A Case Report
Author(s) -
Nik Adilah Nik Othman,
Nur Saadah Mohamad,
Ahmad Aizuddin Mohamad Jamali,
M.J. Abdullah,
Mohd Khairi Md Daud
Publication year - 2021
Publication title -
international medical journal malaysia/iium medical journal malaysia
Language(s) - English
Resource type - Journals
eISSN - 2735-2285
pISSN - 1823-4631
DOI - 10.31436/imjm.v20i4.1757
Subject(s) - medicine , sensorineural hearing loss , abnormality , palsy , audiology , hearing loss , auditory canal , facial nerve , surgery , pathology , alternative medicine , psychiatry
Duplication of the internal auditory canal is a rare entity. It can be unilateral or bilateral involvement and usually found during an investigation of sensorineural hearing loss or facial nerve palsy. We report this image finding in a child with Down syndrome with bilateral profound sensorineural hearing loss. There was no facial nerve palsy. We highlight the rarity of this image finding and the importance of imaging for detection of middle and inner ear abnormality in a case of congenital sensorineural hearing loss as it helps in decision making for the suitable treatment.
Keywords: Duplicate IAC; Bilateral Duplicate IAC; sensorineural hearing loss; Down syndrome