Open AccessDyke-Davidoff-Masson Syndrome with crossed cerebellar atrophy
Author(s) -
Ramesh Kumar,
Deepak Kumar,
Himanshu Mishra,
Sanjay Kumar Suman,
Umakant Prasad
Publication year - 2021
Publication title -
nepal journal of neuroscience
Language(s) - English
Resource type - Journals
eISSN - 1813-1956
pISSN - 1813-1948
DOI - 10.3126/njn.v18i3.37163
Subject(s) - atrophy , anatomy , cerebral atrophy , facial symmetry , cerebellum , medicine , cerebellar hemisphere , pathology , psychology , surgery
Dyke-Davidoff-Masson Syndrome (DDMS) is a rare neurological condition characterised clinically by recurrent seizures, facial asymmetry, hemiplegia and mental retardation likely due to foetal or early childhood cerebral insult. We describe the MRI findings of DDMS in a 10-year-old male child. MRI brain revealed right cerebral atrophy, ipsilateral thickening of calvarium, right lateral ventricular dilatation, hyper-pneumatisation of frontal sinus, and contralateral cerebellar atrophy which are consistent with DDMS.