Open AccessMixed Variant of Acrokeratosis verruciformis of Hopf: A rare entity
Author(s) -
Sonia Jain,
Pratiksha Sonkusale,
Abhay Vilas Deshmukh,
Pallavi Kumari
Publication year - 2021
Publication title -
nepal journal of dermatology, venereology and leprology
Language(s) - English
Resource type - Journals
eISSN - 2091-167X
pISSN - 2091-0231
DOI - 10.3126/njdvl.v19i2.37813
Subject(s) - genodermatosis , histopathology , etiology , lesion , dorsum , dermatology , medicine , pathology , anatomy , biology , genetics , gene
Acrokeratosis verruciformis of Hopf (AKV) is a rare autosomal dominant genodermatosis of unknown etiology. Here we present a case of a 20-year-female with multiple skin-colored flat papules over the dorsum of hands and feet interspersed with multiple hypopigmented macular lesions of 5 years duration. No family member showed a similar lesion. The presence of classical AKV with absent family history and definite histopathology findings make this case an unusual and rare entity.