Open AccessCongenital Cystic Adenomatoid Malformation of the Lung: A Case Report
Author(s) -
Mangla Sood
Publication year - 1970
Publication title -
journal of nepal paediatric society
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.13
H-Index - 8
eISSN - 1990-7982
pISSN - 1990-7974
DOI - 10.3126/jnps.v31i1.4162
Subject(s) - medicine , congenital cystic adenomatoid malformation , lung , respiratory distress , gestation , amniotic fluid , mediastinal shift , pediatrics , pathology , fetus , pregnancy , radiology , biology , genetics
Congenital cystic adenomatoid malformations (CCAM) of the lung are rare congenital cystic lung lesions that arise from excessive disorganized proliferation of tubular bronchial structures. The prenatal rate of detection of lung cysts at the routine 18–20-week scan is almost 100%.However as gestation progresses the tracheobronchial tree becomes patent and the fl uid within the cysts exits into the amniotic fl uid and the cysts collapse, allowing the other lobes of the lung to develop normally. Only at birth do the cysts then expand and present in the newborn period with respiratory distress. In late childhood or in adult life, it can present as recurrent chest infections or even undergo malignant transformation. We report a case of Type II CCAM in newborn with brief review of literature. DOI: 10.3126/jnps.v31i1.4162J Nep Paedtr Soc 2010;31(1):64-67