Open AccessA young man with progressive jaundice and abdominal distension
Author(s) -
Sith Siramolpiwat,
Tanabute Limprukkasem
Publication year - 2019
Publication title -
thai journal of hepatology
Language(s) - English
Resource type - Journals
ISSN - 2586-9833
DOI - 10.30856/th.jhep2019vol2iss1_02
Subject(s) - budd–chiari syndrome , medicine , ascites , abdominal distension , jaundice , abdomen , radiology , portal hypertension , liver disease , muscle hypertrophy , surgery , gastroenterology , cirrhosis , inferior vena cava
Budd-Chiari syndrome (BCS) is a rare, life-threatening disease caused by obstruction of hepatic venous outflow. Common presentations are right upper quadrant pain, ascites, and hepatomegaly. A diagnosis of Budd-Chiari syndrome should be suspected when liver disease occurs in a patient with known risk factors for hypercoagulable state. We report a 22-years old transgender man presented with jaundice, marked ascites and hepatomegaly. Imaging studies showed complete thrombosis of all hepatic veins. Finally, he was diagnosed with Budd-Chiari syndrome with antiphospholipid syndrome.
Figure 1 ภาพ CT upper abdomen แสดงให้เห็น marked ascites with heterogeneous liver enhancement, complete obliteration of all hepatic, caudate lobe hypertrophy, small intrahepatic venous collateral และ small arterial enhancing nodules