Open AccessBilateral idiopathic optic nerve sheath meningocele: A case report and literature review
Author(s) -
Alberto Morello,
Andrea Bianconi,
Maurizio Cogoni,
Silvana Borgarello,
Diego Garbossa,
Barbara Massa Micon
Publication year - 2022
Publication title -
journal of neurosciences in rural practice
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.331
H-Index - 22
eISSN - 0976-3147
pISSN - 0976-3155
DOI - 10.25259/jnrp_5_2022
Subject(s) - medicine , acetazolamide , fenestration , optic nerve , surgery , cerebrospinal fluid , ophthalmology , anesthesia , pathology
Optic nerve (ON) sheath meningocele is an enlargement of the ON sheath, consisting in a cerebrospinal fluid collection along the perineural space of the optic nerve. It should be considered primary when it is not associated with orbital-cerebral neoplasm or with cranio-orbital junction malformations. Here, we report a case of bilateral primary idiopathic ON meningocele with gradual vision loss, treated with acetazolamide, which showed a maintained visual recovery and partial improvement during a 6-month follow-up period. The literature review retrieved eight cases of primary idiopathic ON sheath meningocele: ON sheath fenestration is considered in patients with progressive and severe vision loss, otherwise, acetazolamide treatment is indicated with good results on symptoms control, as confirmed in our case report.