Open AccessSurgical approach and prognosis of primitive chest wall alveolar rhabdomyosarcoma in an adult: A case report and review of the literature
Author(s) -
Narindra Njarasoa Mihaja Razafimanjato,
T.D.N. Ravelomihary,
Mampioa Ranaivomanana,
Guillaume Odilon Tsiambanizafy,
Hanitrala Jean Louis Rakotovao,
Francis Allen Hunald
Publication year - 2020
Publication title -
journal of clinical and investigative surgery
Language(s) - English
Resource type - Journals
ISSN - 2559-5555
DOI - 10.25083/2559.5555/5.2/104.108
Subject(s) - medicine , rhabdomyosarcoma , alveolar rhabdomyosarcoma , thoracic wall , presentation (obstetrics) , surgery , resection , genitourinary system , surgical resection , radiology , sarcoma , anatomy , pathology
Alveolar rhabdomyosarcomas (ARMS) are rare entities that occur predominantly on the extremities and represent 20% of rhabdomyosarcomas. Other common locations include the peri-rectal and perineal regions, head and neck, and genitourinary system. To our knowledge, this presentation is the first case of alveolar rhabdomyosarcoma of the chest wall reported in the literature. Here, we describe a case of a 64-year-old man with alveolar rhabdomyosarcomas who underwent a chest wall resection. The defect was reconstructed with polypropylene mesh and latissimus dorsi muscle. Our patient did not show recurrence ten months after complete resection. The present paper describes our surgical approach to a case of primary alveolar rhabdomyosarcoma of the chest wall in an adult. The authors discuss the principal judgment criteria for successful surgical resection and prognosis, highlighting the relevance of chest wall reconstruction and their complementary aspects in the multimodal management of this rare entity.