Open AccessPityriasis rubra pilaris: report of a rare case
Author(s) -
Carolina Oldoni,
Beatriz Maria Vilaça,
Fernanda Nomoto Fujii,
Leticia Andrade,
Maira Mitsue Mukai
Publication year - 2021
Publication title -
residência pediátrica
Language(s) - English
Resource type - Journals
ISSN - 2236-6814
DOI - 10.25060/residpediatr-2021.v11n1-110
Subject(s) - pityriasis rubra pilaris , medicine , dermatology , isotretinoin , trunk , skin biopsy , erythroderma , psoriasis , biopsy , pathology , ecology , biology , acne
OBJECTIVES: Report the case of pityriasis rubra pilaris (PRP) in a male patient at the age of 2 years and 10 months. METHODS: A review of the medical record as well as the literature regarding the present conditions, via PubMed database. RESULTS: Male patient, 2 years and 10 months, referred for the first year of appearance of pruritic erythematodescamative annular plaques in lower limbs with dissemination to the trunk, upper limbs, and face, associated with scaling in the plantar region and nail dystrophy. The biopsy presented stratum corneum parakeratotic with hypergranulosis and moderate acanthosis. The diagnosis of pityriasis rubra pilaris was considered conclusive. Isotretinoin and oral antihistamine were prescribed, having complete improvement. CONCLUSIONS: PRP remains a challenging disease, be it on its pathogeny, diagnosis or treatment. Randomized studies would aid on establishing a standardized treatment for PRP, improving the quality of life of patients suffering from this disease.