Open AccessTHE COMBINATION OF ANNULAR PANCREAS, PARASTERNAL DIAPHRAGMATIC HERNIA IN A NEWBORN WITH DOWN SYNDROME
Author(s) -
M.A. Akselrov,
В. А. Емельянова
Publication year - 2018
Publication title -
vestnik hirurgii im. i.i. grekova/vestnik hirurgii imeni i.i. grekova
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.136
H-Index - 7
eISSN - 2686-7370
pISSN - 0042-4625
DOI - 10.24884/0042-4625-2018-177-4-44-46
Subject(s) - medicine , parasternal line , annular pancreas , congenital diaphragmatic hernia , diaphragmatic hernia , duodenal atresia , diaphragmatic breathing , down syndrome , abnormality , duodenum , pediatrics , surgery , hernia , fetus , pathology , atresia , pregnancy , alternative medicine , psychiatry , biology , genetics
Malformations and premature birth are the most important causes of chronic diseases, disability and mortality in childhood. Help for children with malformations is often needed immediately after birth. WHO determines heart defects, neural tube defects, chromosomal abnormality – Down syndrome as the most severe malformations. Down syndrome is a genetic disease in which the child has the superfluous chromosome and often defects in the development of different organs and systems. The presence of several defects requires a complex surgical approach that can be performed endoscopically. It is known that Down syndrome can be combined with chyloperitoneum. The article represents the clinical observation of successful treatment of the newborn baby with Down syndrome, which was combined with congenital high intestinal obstruction at the level of the duodenum and parasternal diaphragmatic hernia, both defects were corrected laparoscopically. The chyloperitoneum developed in postoperative period was successfully treated with the appointment of total parenteral nutrition and infusions of Sandostatin analogues.