Open AccessParry-Romberg, un síndrome neurocutáneo: presentación de tres casos
Author(s) -
Arturo Olvera-Acevedo,
Paulina Carreño-Pérez,
Nedelé Zaldívar-López,
Benjamín Medina-Fonseca,
Alma Duarte-García
Publication year - 2021
Publication title -
revista medica del instituto mexicano del seguro social/revista médica del instituto mexicano del seguro social
Language(s) - Spanish
Resource type - Journals
eISSN - 2448-5667
pISSN - 0443-5117
DOI - 10.24875/rmimss.m20000042
Subject(s) - parry , humanities , philosophy , computer science , artificial intelligence
Parry-Romberg syndrome is characterized by progressive hemiatrophy of the skin, subcutaneous tissue, muscle and bones of the skull. Its incidence is low, with a progressive and slow course. Its etiology is unknown, but it has been associated with several factors. Its clinical presentation involves dermatological, musculoskeletal and neuropsychiatric manifestations. The treatment consists of medical and surgical strategies. The use of steroids, alone or in combination with immunomodulators, has the objective of slowing down progression. The surgical treatment lies in facial reconstruction or volumetric regeneration, to correct the appearance and function of facial structures. The objective is to show three cases of Parry-Romberg syndrome with the representative characteristics of the disease.