Open AccessVon Meyenburg complex associated with adult polycystic liver disease
Author(s) -
Dušan Lalošević,
P Milosević,
Nada Vučković,
V Uzurov,
Zlatibor Andjelković,
Matilda Djolai
Publication year - 2005
Publication title -
medicinski pregled
Language(s) - English
Resource type - Journals
eISSN - 1820-7383
pISSN - 0025-8105
DOI - 10.2298/mpns0504191l
Subject(s) - medicine , cyst , polycystic liver disease , pathology , connective tissue , bile duct , parenchyma , polycystic disease , asymptomatic , polycystic kidney disease , biopsy , hamartoma , kidney , disease , surgery , transplantation , liver transplantation
The von Meyenburg complex (bile duct hamartoma) is a rare developmental disorder, manifested by multiple bile ducts. The polycystic liver disease is a rare congenital anomaly which may remain undiscovered until adult life, occurring more frequently in women. It is mostly asymptomatic, but sometimes surgical intervention is necessary. In the majority of cases, it is combined with cysts in the kidney and, rarely, in other organs as well. The cysts may vary in diameter from 1 mm to 20 cm, or even more.