Open AccessStenosis due to inflammatory bowel disease in patient with glycogenosis Ib-the rapeutical options
Author(s) -
Tamara Alempijević,
Ivan Jovanović,
Miloš Štulić,
Danica Pejkovic-Stamenkovic,
Predrag Miljić,
Biljana Miličić,
Marjan Micev,
Dragana Popović,
Sanja Mijatović,
S Krstić,
Aleksandar Karamarković
Publication year - 2013
Publication title -
acta chirurgica iugoslavica
Language(s) - English
Resource type - Journals
eISSN - 2406-0887
pISSN - 0354-950X
DOI - 10.2298/aci1304091a
Subject(s) - medicine , inflammatory bowel disease , ileus , stenosis , disease , surgery , gastroenterology
The occurrence of inflammatory bowel disease in patients with glycogen storage disease Ib is rare (GSDIb).We present the case of a young woman with the diagnosis of GSD-Ib Crohn-like colitis developed at age 27. She was under regular medical control because of severe malnutrition, secondary amenorrhea, leukopenia, neutropenia, hyperlipidaemia, dysfunctions of phagocytosis, and a subtotal stenosis of the ascending colon. Several months after diagnosing Crohn-like colitis, symptoms and signs of ileus developed, and she was admitted in the Emergency room department. Baloon dilatation with local corticosteroid injection was used for treatment. Clinical status of the patient markedly improved after this intervention. As far as we know, no similar cases with this kind of treatment are published.