Open AccessUnusual presentation of dermatofibrosarcoma protuberans
Author(s) -
Tobias A. Mattei,
Ricardo Ramina,
Paulo Henrique Pires de Aguiar,
Jerônimo Buzetti Milano,
Daniel Pereira Mandarino
Publication year - 2018
Publication title -
jornal brasileiro de neurocirurgia
Language(s) - English
Resource type - Journals
eISSN - 2446-6786
pISSN - 0103-5118
DOI - 10.22290/jbnc.v18i1.627
Subject(s) - dermatofibrosarcoma protuberans , medicine , presentation (obstetrics) , dermatofibrosarcoma , lesion , skull , sarcoma , transposition (logic) , surgery , dermatology , pathology , linguistics , philosophy
Dermatofibrosarcoma protuberans is a rare neoplasm, usually presenting as a low-grade, non-invasive, slow-growing tumor, with a pronounced tendency to local recurrence. We present a rare case of a high-grade, histologically undifferentiated lesion, which eroded underlying bony structures. A wide local excision with careful pathologic analysis of margins was performed with immediate reconstruction of skull bone and musculo-cutaneous flap transposition in order to cover the skin defect. A one-stage surgical procedure, such as presented in this report, is the treatment of choice recommended by the authors.