Open AccessCase of congenital adrenocortical cancer
Author(s) -
Л. Р. Карасева,
Lyudmila Privalova,
Е. Г. Новопольцева,
В. В. Радовский
Publication year - 2019
Publication title -
rossijskij žurnal detskoj gematologii i onkologii
Language(s) - English
Resource type - Journals
eISSN - 2413-5496
pISSN - 2311-1267
DOI - 10.21682/2311-1267-2019-6-2-76-79
Subject(s) - medicine , adrenocortical carcinoma , sepsis , cancer , hypertrophic cardiomyopathy , childhood cancer , pediatrics , surgery , cardiology
The article presents a unique clinical observation of adrenocortical cancer (ACC) in a newborn baby, whose mother suffered from a recurrent form of maxillary fibrosarcoma and had a burdened obstetric and gynecological history, but was not examined by a geneticist. Complications of ACC in the presented patient were secondary hypertrophic cardiomyopathy with obstruction of the exit paths of both ventricles, Itsenko– Cushing syndrome. Despite the surgical treatment carried out according to vital indications (tumoradinectomy on the right with hormonal support with a Solu-Cortef), the child died during the progression of multiple organ failure and sepsis.