Open AccessTHE COMPLEXITY OF DIAGNOSING IDIOPATHIC PULMONARY ARTERIAL HYPERTENSION
Author(s) -
Д. И. Садыкова,
Д. Р. Сабирова,
Natalya Kustova,
Н. Н. Фирсова,
Г. А. Хуснуллина
Publication year - 2018
Publication title -
rossijskij vestnik perinatologii i pediatrii
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.139
H-Index - 4
eISSN - 2500-2228
pISSN - 1027-4065
DOI - 10.21508/1027-4065-2018-63-5-167-171
Subject(s) - medicine , etiology , pulmonary hypertension , cardiology , pulmonary artery , disease , lesion , surgery
Idiopathic pulmonary arterial hypertension is a progressive, incurable disease of unclear etiology; it is characterized by intensive remodeling of the pulmonary vascular bed with a predominant lesion of the distal pulmonary arteries and arterioles. A diagnostic criterion of the disease is an increase in the average pressure in the pulmonary artery more than 25 mm Hg. Arterial hypertension is difficult to diagnose, especially at the early stages due to non-specific clinical symptoms. The article describes the clinical case of diagnostics and treatment of a child with primary pulmonary hypertension of high degree.