Open AccessKimura Disease as a Rare Cause of Proptosis: A Case Report
Author(s) -
V Sha Kri Eh Dam,
Irfan Mohamad,
Evelyn Li Min Tai,
Adil Hussein,
Khairil Amir Sayuti,
Fatihatul Munirah Amiruddin,
Faezahtul Arbaeyah Hussain
Publication year - 2021
Publication title -
archives of orofacial sciences/archives of orofacial science
Language(s) - English
Resource type - Journals
eISSN - 2231-7163
pISSN - 1823-8602
DOI - 10.21315/aos2021.16.2.15
Subject(s) - medicine , etiology , kimura's disease , head and neck , prednisolone , rare disease , presentation (obstetrics) , lymphoma , dermatology , disease , lymph node , surgery , pathology
Kimura disease (KD) is a rare chronic inflammatory disorder of unknown aetiology that primarily affects the head and neck region with lymph node involvement. Young to middle-aged adult Asian males are predominantly affected. The most common presentation is painless subcutaneous swelling in the head and neck region, while proptosis or orbital involvement is very rarely reported. KD shares some features with other inflammatory and neoplastic disorders, including lymphoma; thus, investigations to confirm the diagnosis should not be delayed. Systemic corticosteroids are commonly used to treat KD and show an excellent response; however, the optimal treatment is still uncertain, and KD has a high recurrence rate. We describe the case of a patient with KD who presented with proptosis and post-auricular swelling, which responded well to oral prednisolone treatment.