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Infantile Genetic Agranulocytosis (Kostmann Type). A Case Report
Author(s) -
Saǧlam Funda,
Atamer Tanju,
Onan Utku,
Soydinç Mahtaban,
Kiraç Kaan
Publication year - 1995
Publication title -
journal of periodontology
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 2.036
H-Index - 156
eISSN - 1943-3670
pISSN - 0022-3492
DOI - 10.1902/jop.1995.66.9.808
Subject(s) - medicine , neutropenia , curettage , congenital neutropenia , genetic syndromes , dermatology , pediatrics , pathology , chemotherapy
S evere periodontitis in a patient with infantile genetic agranulocytosis (Kostmann syndrome) is presented. This rare syndrome is inherited as an autosomal recessive pattern and characterized by severe neutropenia. The periodontal status and treatment of the patient is described. It is concluded that periodontal therapy including scaling, root planing, soft tissue curettage, and the use of selected antimicrobial agents can be successful in this particular syndrome. J Periodontol 1995;66:808–810 .