
Disseminated Juvenile Pilomyxoid Astrocytoma of the HypothalamicChiasmatic Region
Author(s) -
Ahmet Mesrur Halefoğlu,
Begüm Özel
Publication year - 2020
Publication title -
acta medica iranica.
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.218
H-Index - 27
eISSN - 1735-9694
pISSN - 0044-6025
DOI - 10.18502/acta.v57i9.2643
Subject(s) - medicine , pilocytic astrocytoma , magnetic resonance imaging , astrocytoma , radiology , regimen , pathology , glioma , cancer research
Pilomyxoid astrocytoma (PMA) is a recently described histological type of pilocytic astrocytoma (PA), but the tumors show histological differences. PMA has more aggressive malignant behavior than PA. Magnetic Resonance Imaging (MRI) may play a crucial role in the preoperative setting and also help to establish an appropriate therapeutic regimen. In this case report, we illustrated MRI findings of a hypothalamic-chiasmatic PMA in a 15-year-old female patient presenting with extensive leptomeningeal seeding. The patient was operated for total tumor resection, but could not survive the second post-operative day. We have comprehensively discussed the clinical, imaging, and histopathological features of these relatively rare tumors and also reviewed the recent literature.