Low grade appendiceal mucinous neoplasm

Low grade appendiceal mucinous neoplasm (LAMN) is a rare tumour which lacks usual form of destructive invasion but has ability to spread to peritoneum and ovaries which frequently progresses to pseudomyxoma peritonei and often result in death of patient despite the bland histology of the mucinous epithelium. There are lot of controversies about its classification, clinical significance of pseudomyxoma peritonei, whether ovarian mucinous tumours in this setting are separate primaries or are the metastasis from the appendiceal tumours which are to be solved. We reported two cases of LAMN in which first case was with pseudomyxoma peritonei with secondary involvement of left ovary while other was simple LAMN without any involvement. Whenever we diagnosed LAMN it is necessary to look for ovarian involvement and pseudomyxoma peritonei. It is necessary to rule out ovarian involvement and pseudomyxoma peritonie whenever we diagnosed LAMN. The unified approach of grading pseudomyxoma peritonei is required for more standardized and prognostically valuable diagnostic reporting.