Open AccessThe age-related assessment of pulmonary function in children with cystic fibrosis aged below 6 years
Author(s) -
Е. Г. Фурман,
Е. И. Кондратьева,
A. V. Chernyak,
V. Shadrina
Publication year - 2020
Publication title -
pulʹmonologiâ
Language(s) - English
Resource type - Journals
eISSN - 2541-9617
pISSN - 0869-0189
DOI - 10.18093/0869-0189-2019-29-6-739-744
Subject(s) - cystic fibrosis , pulmonary function testing , medicine , disease , pediatrics , pulmonary fibrosis , pulmonary disease , intensive care medicine , fibrosis
Cystic fibrosis (CF) is a severe hereditary disease associated with progressive impairment of respiratory organs. Pulmonary function test (PFT) in CF patients may be relevant for determination of therapy level and patient management strategy. However, PFT is particularly difficult in children aged below 6 years. Literature data concerning options for pulmonary function analysis in children aged below 6 years with CF for assessment of disease severity, progression and monitoring of treatment efficacy are provided in the article.