Open AccessDiagnosis of Osteofibrous Dysplasy in Children
Author(s) -
А. И. Снетков,
G N Berchenko,
O. L. Nechvolodova,
L. F. Savkina
Publication year - 1998
Publication title -
vestnik travmatologii i ortopedii imeni n.n. priorova
Language(s) - English
Resource type - Journals
eISSN - 2658-6738
pISSN - 0869-8678
DOI - 10.17816/vto104382
Subject(s) - medicine , tibia , deformity , radiology , anatomy
The first description in Russian literature of osteofibrous dysplasy in children is presented. It is grounded on the analysis of diagnostic peculiarities and treatment of 24 patients in the period from 1966 to 1996 The main diagnostic criteria by clinical, radiologic and pathomorphologic features are given. Osteofibrous dysplasy is a rare and insufficiently studied disease affecting mainly tibia in children of the first ten years. It has dysplastic congenital nature and is similar to the biastomatosis process. Saber-like deformity of the affected segment prevails in clinical picture. This deformity may be of different degree of manifestation and accompanied by painless. Eccentric intracortical location of pathologic focus is typical of radiologic picture. Morphologic examination is the main diagnostic method. Histologic study shows architectonics zone of the pathologic focus which consists of fibrous tissue with bone trabeculae inclusion (bone trabeculae with laminar structure) mainly surrounded by active osteoblasts.