Open AccessCongenital localized pulmonary emphysema in children
Author(s) -
M. R. Rokytsky,
R. V. Khabibullina,
V. N. Poryvaeva,
П. Н. Гребнев
Publication year - 1989
Publication title -
kazanskij medicinskij žurnal
Language(s) - English
Resource type - Journals
eISSN - 2587-9359
pISSN - 0368-4814
DOI - 10.17816/kazmj101579
Subject(s) - congenital lobar emphysema , medicine , pulmonary emphysema , lung , parenchyma , disease , bronchus , anatomy , pathology , respiratory disease
Congenital lobar emphysema, or progressive emphysema of newborns, is a malformation associated with incomplete patency of the bronchus and the formation of a valve mechanism in it as a result of cartilage development defects and is caused by segmental or lobar ballooning of the lung parenchyma. The term "congenital localized emphysema" should obviously be recognized as the most rational one, since not only one lobe, but also separate segments and several lobes can be affected by this disease. It occurs relatively rarely in children, so the causes of its occurrence have not been studied enough so far. Due to the rarity of the disease, as well as a small number of publications, diagnostic errors and adverse outcomes are possible.