Clinical Mechanism of the Cystic Fibrosis Transmembrane Conductance Regulator Potentiator Ivacaftor in G551D-mediated Cystic Fibrosis
Author(s) -
Steven M. Rowe,
Sonya L. Heltshe,
Tanja Gonska,
Scott H. Donaldson,
Drucy Borowitz,
Daniel Gelfond,
Scott D. Sagel,
Umer Khan,
Nicole MayerHamblett,
Jill M. Van Dalfsen,
Elizabeth Joseloff,
Bonnie W. Ramsey
Publication year - 2014
Publication title -
carolina digital repository (university of north carolina at chapel hill)
Language(s) - English
DOI - 10.17615/6390-mp35
Subject(s) - ivacaftor , potentiator , cystic fibrosis , cystic fibrosis transmembrane conductance regulator , regulator , mechanism (biology) , medicine , conductance , chemistry , pharmacology , physics , biochemistry , gene , quantum mechanics , condensed matter physics
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