Premium
Adult‐onset Rasmussen encephalitis associated with focal cortical dysplasia
Author(s) -
Hohenbichler Katharina,
Lelotte Julie,
Lhommel Renaud,
Tahry Riëm El,
Vrielynck Pascal,
Santos Susana Ferrao
Publication year - 2017
Publication title -
epileptic disorders
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.673
H-Index - 53
eISSN - 1950-6945
pISSN - 1294-9361
DOI - 10.1684/epd.2017.0947
Subject(s) - cortical dysplasia , encephalitis , medicine , pathology , dysplasia , epilepsy , virology , virus , psychiatry
Rasmussen encephalitis is a rare, devastating condition, typically presenting in childhood. Cases of adult‐onset Rasmussen have also been described, but the clinical picture is less defined, rendering final diagnosis difficult. We present a case of adult‐onset Rasmussen encephalitis with dual pathology, associated with focal cortical dysplasia and encephalitis. We interpreted the Rasmussen encephalitis to be caused by severe and continuous epileptic activity due to focal cortical dysplasia. The best therapeutic approach for such cases remains unclear.