
Spectrum of Presentations and Management Strategies in Renal Angiomyolipoma
Author(s) -
Sinan Khaddam,
Shuchi Gulati
Publication year - 2022
Publication title -
journal of kidney cancer and vhl
Language(s) - English
Resource type - Journals
ISSN - 2203-5826
DOI - 10.15586/jkcvhl.v9i1.221
Subject(s) - tuberous sclerosis , angiomyolipoma , lymphangioleiomyomatosis , medicine , pathology , kidney , intensive care medicine
Renal angiomyolipoma (rAML) occurs rarely sporadically but is commonly encountered in patients with tuberous sclerosis complex and lymphangioleiomyomatosis. rAML is a rare entity, not seen regularly in daily practice; however, is commonly encountered and diagnosed by clinicians who approach and treat kidney masses. Basic knowledge of this entity is necessary to recognize that despite being benign, these tumors can rarely cause deadly complications such as hemorrhage or severe renal dysfunction or may have malignant components associated with them.