Open AccessDyke-Davidoff-Masson Syndrome: A Delayed Diagnosis of an Acquired Variant
Author(s) -
T. Seetam Kumar,
Abhijit Vipul,
Rohitash Yadav
Publication year - 2018
Publication title -
journal of medical research and innovation
Language(s) - English
Resource type - Journals
ISSN - 2456-8139
DOI - 10.15419/jmri.121
Subject(s) - neuroimaging , intractable epilepsy , hemiparesis , epilepsy , thickening , medicine , psychology , neuroscience , pediatrics , surgery , lesion , chemistry , polymer science
Dyk-Davidof-Masson Syndrome (DDMS) is an important cause of intractable and drug-resistant seizures. It has varied clinical presentation and history with distinct neuroimaging features. Here, we describe a female patient presented with recurrent intractable convulsion, mental retardation, hemiparesis, and characteristic neuroimaging features of cerebral hemiatrophy, calvarial thickening, and ipsilateral hyperpneumatization of the frontal sinuses which is suggestive of DDMS. Early institution of neuroimaging in patients with intractable epilepsy will make early diagnosis and better outcome.