Open AccessFibrosing arthropathy in juvenile scleroderma
Author(s) -
Д. А. Дибров,
M. N. Starovoytova,
O. Desinova
Publication year - 2021
Publication title -
sovremennaâ revmatologiâ
Language(s) - English
Resource type - Journals
eISSN - 2310-158X
pISSN - 1996-7012
DOI - 10.14412/1996-7012-2021-2-64-68
Subject(s) - scleroderma (fungus) , medicine , localized scleroderma , morphea , systemic scleroderma , dermatology , muscle contracture , disease , differential diagnosis , systemic disease , pathology , multisystem disease , fibrosis , surgery , lichen sclerosus , inoculation
The group of scleroderma diseases includes a number of clinical entities, the main symptom of which is skin tightening. Scleroderma is a prominent example of these diseases, characterized by excessive synthesis and deposition of collagen in organs and tissues. A patient with juvenile systemic scleroderma with induration of the skin and underlying tissues, and persistent contractures of large joints since childhood, is described. This clinical example illustrates disease course peculiarities and differential diagnosis of systemic and limited (focal) scleroderma and scleroderma-like conditions in pediatric patients. The feasibility of pathogenetic therapy aimed at improving patient's the quality of life with formed disease phenotype is shown.