Open AccessAtypical Retinoblastoma Presentation - A Challenge for the Treating Ophthalmologist
Author(s) -
Siti Amra Abd Rahman,
Ahmad Salehuddin Mohammad,
Safinaz Mohd Khialdin,
Siti Norzalehawati Sepain Jusoh
Publication year - 2021
Publication title -
journal of evolution of medical and dental sciences
Language(s) - English
Resource type - Journals
eISSN - 2278-4802
pISSN - 2278-4748
DOI - 10.14260/jemds/2021/720
Subject(s) - medicine , retinoblastoma , presentation (obstetrics) , malignancy , strabismus , incidence (geometry) , ophthalmology , glaucoma , pediatrics , surgery , biochemistry , chemistry , physics , optics , gene
Retinoblastoma is the most common primary intraocular malignancy in children.1 Incidence of retinoblastoma is constant worldwide at one case per 15000–20000 live births, which corresponds to about 9000 new cases every year.2,3 It usually occurs in children under five years of age and can lead to loss of vision, and in extreme cases, death.4 The common signs of its presentation are leukocoria, strabismus, secondary glaucoma, proptosis, anterior chamber inflammatory signs and spontaneous hyphaema.1 Prognosis for vision and survival has significantly improved due to timely diagnosis and improved treatment methods.5