Open AccessNurses' knowledge about Berardinelli-Seip Congenital Lipodystrophy
Author(s) -
Verônica Kristina Cândido Dantas,
Joice da Silva Soares,
Lázaro Batista de Azevedo Medeiros,
Aquiles Sales Craveiro Sarmento,
Thaíza Teixeira Xavier Nobre,
Fábia Barbosa de Andrade,
Josivan Gomes Lima,
Julliane Tamara Araújo de Melo Campos
Publication year - 2018
Publication title -
plos one
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.99
H-Index - 332
ISSN - 1932-6203
DOI - 10.1371/journal.pone.0197784
Subject(s) - lipodystrophy , medicine , health professionals , family medicine , disease , pediatrics , health care , human immunodeficiency virus (hiv) , viral load , antiretroviral therapy , economics , economic growth
Berardinelli-Seip Congenital Lipodystrophy (BSCL) is a rare autosomal recessive disease characterized by the almost complete absence of adipose tissue. Due to a strong founder effect that resulted in a higher prevalence of BSCL in Rio Grande do Norte ( RN ), a state in northeastern Brazil, it has been essential that health professionals develop knowledge about this disease. Nurses are often the first point of contact with patients during health care assistance. The purpose of this study was to investigate the knowledge of these professionals about BSCL in two main hospitals in RN state. A questionnaire was applied to 199 nurses working in the Hospital Regional Mariano Coelho — HRMC (Regional Hospital Mariano Coelho), in Currais Novos–RN , and in the Hospital Universitário Onofre Lopes — HUOL (University Hospital Onofre Lopes), in Natal–RN . This study showed that most nursing professionals do not know about the disease, although they have already received patients with BSCL in those hospitals. The nurses from HRMC and HUOL lacked knowledge of BSCL and the healthcare of these patients requires immediate improvement. Significant efforts are required to close the gap between current and needed practice patterns.