Open AccessRespiratory failure after scoliosis correction surgery in patients with Prader-Willi syndrome: Two case reports
Author(s) -
Ju-Yul Yoon,
Sung-Hee Park,
Yu Hui Won
Publication year - 2021
Publication title -
world journal of clinical cases
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.368
H-Index - 10
ISSN - 2307-8960
DOI - 10.12998/wjcc.v9.i32.9960
Subject(s) - medicine , hypoventilation , scoliosis , polysomnography , hypercapnia , respiratory failure , obstructive sleep apnea , respiratory monitoring , pulmonary function testing , obesity hypoventilation syndrome , respiratory system , anesthesia , apnea , pediatrics , surgery
Sleep-disordered breathing, including hypoventilation and obstructive sleep apnea, is often observed in Prader-Willi syndrome (PWS). Particularly in adolescence, scoliosis causes a progressive restrictive pulmonary pattern, leading to hypoventilation, so timely corrective surgery is required. However, the effect is controversial. In addition, since mental retardation of PWS, patient effort-based respiratory tests may be less reliable. So far, no studies have accurately reported on the comparison of respiratory function before and after corrective surgery, and appropriate respiratory function measurement method in PWS.