Open AccessTuberous sclerosis complex-lymphangioleiomyomatosis involving several visceral organs: A case report
Author(s) -
Hongbin Chen,
Xinyu Xu,
CaiGui Yu,
Mengting Wan,
Chuangli Feng,
Zhi-Yu Zhao,
Dan′e Mei,
Jinling Chen
Publication year - 2021
Publication title -
world journal of clinical cases
Language(s) - Uncategorized
Resource type - Journals
SCImago Journal Rank - 0.368
H-Index - 10
ISSN - 2307-8960
DOI - 10.12998/wjcc.v9.i24.7085
Subject(s) - medicine , tuberous sclerosis , lymphangioleiomyomatosis , pathology , dermatology , anatomy
Lymphangioleiomyomatosis (LAM) is a rare cystic lung disease characterized by the proliferation, metastasis, and infiltration of smooth muscle cells in the lung and other tissues, which can be associated with tuberous sclerosis complex (TSC). The disorder of TSC has a variable expression, and there is great phenotypic variability.