Open AccessCronkhite-Canada syndrome with steroid dependency: A case report
Author(s) -
Dan Jiang,
Guping Tang,
Ming-Yu Lai,
Zhenning Huang,
Zhihai Liang
Publication year - 2021
Publication title -
world journal of clinical cases
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.368
H-Index - 10
ISSN - 2307-8960
DOI - 10.12998/wjcc.v9.i14.3466
Subject(s) - medicine , dependency (uml) , steroid , dermatology , artificial intelligence , hormone , computer science
Cronkhite-Canada syndrome (CCS) is a rare nonhereditary disease characterized by chronic diarrhoea, diffuse gastrointestinal polyposis and ectodermal manifestations. The lethality of CCS can be up to 50% if it is untreated or if treatment is delayed or inadequate. More than 35% of the patients do not achieve long-term clinical remission after corticosteroid administration, with relapse occurring during or after the cessation of glucocorticoid use. The optimal strategy of maintenance therapy of this disease is controversial.