Open AccessType I congenital extrahepatic portosystemic shunt treated by orthotopic liver transplantation: A case report
Author(s) -
Wen Xiang,
Hao Wang,
Zhongzhou Si,
Guang-Shun Chen,
GuanWu Wang,
Ting Li
Publication year - 2019
Publication title -
world journal of clinical cases
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.368
H-Index - 10
ISSN - 2307-8960
DOI - 10.12998/wjcc.v7.i7.903
Subject(s) - medicine , hepatopulmonary syndrome , portosystemic shunt , liver transplantation , transplantation , liver function , radiology , cirrhosis , portal hypertension , surgery , gastroenterology
Congenital extrahepatic portosystemic shunt, also known as Abernethy deformation, is a rare malformation caused by dysplasia in the portal vein system. There are few reports of liver transplantation as a treatment for Abernethy deformation, and our report is the first case in China. This is the second reported case with congenital extrahepatic portosystemic shunt combined with focal nodular hyperplasia and hepatopulmonary treated with liver transplantation.