Open AccessCutaneous Angiosarcoma in an Unusual Location and Without Predisposing Factors
Author(s) -
A. Monteiro,
I. Ferreira,
Artúr César,
Alberto Mota,
Jorge Pinheiro,
J.M. Lopes,
M. Cardoso
Publication year - 2020
Publication title -
european journal of case reports in internal medicine
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.125
H-Index - 1
ISSN - 2284-2594
DOI - 10.12890/2020_001939
Subject(s) - medicine , angiosarcoma , head and neck , dermatology , radiation therapy , soft tissue , biopsy , hemangiosarcoma , immunohistochemistry , disease , skin biopsy , pathology , radiology , surgery
Cutaneous angiosarcoma is a rare, highly malignant tumour of vascular endothelial origin. It usually arises in the skin and superficial soft tissue, mostly on the head and neck. It presents as a variety of lesions, and so is considered a great mimicker, leading to a delay in diagnosis and evidencing the importance of biopsy with immunohistochemistry confirmation. There are few reports of extremity involvement in patients with pre-existing chronic lymphoedema, or exposure to radiation therapy. We report the case of an 82-year-old woman with lower limb extensive cutaneous involvement, distant metastatic disease, and poor therapy response. Its rare location without predisposing factors highlights the need to raise awareness about this disease