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Head and neck manifestation of histiocytosis‐x
Author(s) -
H. Smith Richard J.,
G. Evans John N.
Publication year - 1984
Publication title -
the laryngoscope
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.181
H-Index - 148
eISSN - 1531-4995
pISSN - 0023-852X
DOI - 10.1288/00005537-198403000-00018
Subject(s) - histiocytosis x , medicine , head and neck , histiocytosis , otorhinolaryngology , disease , dermatology , surgery , pathology
Histiocytosis‐X is an uncommon disease, but is relevant to the otolaryngologist because patients with this malady present with, or ultimately develop, head and neck manifestations. Sixty‐two patients with histologically confirmed histiocytosis‐X have been examined at the Hospital for Sick Children in London since 1958. Most patients were under 2 years of age on initial examination and had either osseous or dermatologic disease involvement. Less commonly, otic or oral lesions were found. Histiocytosis‐X is a systemic disease and must be treated accordingly. Isolated lesions may mimic common disease processes, therefore it is imperative that if a seemingly simple problem does not resolve with routine therapy, further patient evaluation be undertaken, If diagnosed, histiocytosis‐X can generally be controlled with Steroid therapy, or in more recalcitrant cases, by the addition of chemotherapy.