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Combined Emphysema and Interstitial Lung Disease as a Rare Presentation of Pulmonary Involvement in a Patient with Chronic Visceral Acid Sphingomyelinase Deficiency (Niemann-Pick Disease Type B)
Author(s) -
Lucyna Opoka,
Dorota Wyrostkiewicz,
Piotr Radwan-Röhrenschef,
Adriana Roży,
Anna TylkiSzymańska,
Witold Tomkowski,
Monika Szturmowicz
Publication year - 2020
Publication title -
american journal of case reports
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 0.247
H-Index - 18
ISSN - 1941-5923
DOI - 10.12659/ajcr.923394
Subject(s) - medicine , bronchoalveolar lavage , pathology , lung , interstitial lung disease , bronchiectasis , air trapping , idiopathic pulmonary fibrosis , acid sphingomyelinase , pulmonary fibrosis , respiratory disease , gastroenterology , fibrosis , sphingomyelin , cholesterol

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