Open AccessHerlyn–Werner–Wunderlich syndrome in a multiparous female
Author(s) -
Harsumeet S. Sidhu,
Prateek Kumar Madaan
Publication year - 2021
Publication title -
bjr case reports
Language(s) - English
Resource type - Journals
ISSN - 2055-7159
DOI - 10.1259/bjrcr.20200132
Subject(s) - uterus didelphys , mesonephric duct , medicine , renal agenesis , presentation (obstetrics) , genitourinary system , agenesis , mullerian ducts , intravenous pyelogram , pelvic pain , primary infertility , menarche , gynecology , radiology , urinary system , infertility , surgery , uterus , anatomy , pregnancy , kidney , genetics , biology
Herlyn–Werner–Wunderlich syndrome is a rare complex congenital anomaly of the urogenital tract involving Mullerian ducts and mesonephric ducts. It is also called OHVIRA syndrome (Obstructed Hemivagina and Ipsilateral Renal agenesis). It is characterized by a triad of uterus didelphys, obstructed hemivagina and ipsilateral renal agenesis. Patients usually present after menarche with pelvic pain, dysmenorrhea, mass, and rarely with primary infertility in later years. We report a case of a multiparous female who presented to the hospital with pain in lower abdomen for the past 2 months and acute retention of urine for 1 day. This is an atypical presentation in a multiparous female that has been described in a single case report so far. 1 Intravenous pyelogram and MRI of the patient revealed uterine didelphys, obstructed right hemivagina causing hematohemicolpos and right renal agenesis. Thorough knowledge of imaging features can enable a radiologist to make a correct diagnosis even in an atypical presentation.