Open AccessMultivessel endovascular therapy for undiagnosed vascular type Ehlers-Danlos syndrome. Successful percutaneous transcatheter coil embolization of hepatic artery pseudoaneurysm with stenting of right renal and iliac arteries in emergency setting
Author(s) -
Lorenzo Paolo Moramarco,
Carlo Alberto Capodaglio,
Pietro Quaretti,
Nicola Cionfoli,
Ilaria Fiorina,
Eliana Disabella,
Antonio D’Agostino,
Mario Urtis,
Eloisa Arbustini
Publication year - 2020
Publication title -
bjr case reports
Language(s) - English
Resource type - Journals
ISSN - 2055-7159
DOI - 10.1259/bjrcr.20200025
Subject(s) - medicine , pseudoaneurysm , percutaneous , surgery , embolization , radiology , ehlers–danlos syndrome , aneurysm
Among Ehlers-Danlos syndromes, the vascular type is the most severe because of its vascular complications. Transcatheter embolization of medium-sized arteries has become the first-line therapy for life-threatening hemorrhage. Ongoing multiple lesions causing hemorrhagic or ischemic complications in the acute phase can challenge patient management. Multivessel endovascular treatment has never been reported. In this study, we report successful single-session treatment by coiling of a ruptured pseudoaneurysm of the hepatic artery with stenting of dissected right renal and iliac arteries in a 46-year-old female. Percutaneous transfemoral approach was gained and sealed with a plug-based closure device. Genetic disease was subsequently confirmed by molecular analysis.