Fibrosing mediastinitis mimicking as chronic pulmonary thromboembolism
Author(s) -
Dimpi Sinha,
Nischal G Kundaragi,
Sudhir Kale,
Sukrity Sharma
Publication year - 2019
Publication title -
bjr|case reports
Language(s) - English
Resource type - Journals
ISSN - 2055-7159
DOI - 10.1259/bjrcr.20190049
Subject(s) - medicine , mediastinum , presentation (obstetrics) , mediastinitis , pulmonary hypertension , radiology , vascular occlusion , surgery
Fibrosing mediastinitis is an uncommon, benign, progressive disorder caused by proliferation of fibrous tissue within mediastinum resulting in encasement of vital mediastinal broncho-vascular structures. Due to its rarity and variable clinical presentation, it is often misdiagnosed. We are presenting a case of fibrosing mediastinitis in an Ethiopian origin young male presenting with pulmonary hypertension due to simultaneous occlusion of pulmonary vein and arteries, clinically misdiagnosed as chronic pulmonary thromboembolism.
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