Open AccessSwyer-James-MacLeod syndrome with unilateral pulmonary fibrosis: a case report
Author(s) -
Omar Abdulla,
J. R. Cain,
John Howells
Publication year - 2017
Publication title -
bjr case reports
Language(s) - English
Resource type - Journals
ISSN - 2055-7159
DOI - 10.1259/bjrcr.20160105
Subject(s) - medicine , bronchiolitis obliterans , pulmonary fibrosis , idiopathic pulmonary fibrosis , bronchiolitis , lung , fibrosis , bronchiolitis obliterans organizing pneumonia , pathology , lung transplantation , respiratory system
Swyer-James-MacLeod syndrome is a rare, complex disease characterized by the radiological finding of unilateral hyperlucent lung due to pulmonary oligaemia and alveolar hyperdistention as a consequence of previous obliterative bronchiolitis (bronchiolitis obliterans). Idiopathic pulmonary fibrosis is a chronic, progressive, fibrosing interstitial pneumonia of unknown cause characterized by bilateral, chronic, progressive and irreversible fibrosis limited to the lungs. We report an interesting case of Swyer-James-MacLeod syndrome affecting one lung and Idiopathic pulmonary fibrosis affecting the contralateral lung.