Open AccessThe Small Midline Occipital Encephalomeningocele: Definition of a Syndrome
Author(s) -
Michael Schlitt,
J. Powell Williams,
Frank O. Bastian,
Stuart F. Smith
Publication year - 1989
Publication title -
neurosurgery/neurosurgery online
Language(s) - English
Resource type - Journals
SCImago Journal Rank - 1.485
H-Index - 34
eISSN - 1081-1281
pISSN - 0148-396X
DOI - 10.1227/00006123-198904000-00022
Subject(s) - falx cerebri , medicine , anatomy , occipital lobe , encephalocele , embryology , occipital bone , tentorium , occipital region , superior sagittal sinus , skull , radiology , surgery , thrombosis
An unusual group of encephalomeningoceles is described. Two children were noted at birth to have a raised area of abnormal skin at the occipital midline. Both of these lesions were found to perforate the superior sagittal sinus and to end between the leaves of the falx cerebri, and to contain a small amount of abnormal cerebral tissue with no connection to either occipital lobe. Previous case reports are reviewed; these lesions are true encephalomeningoceles, rather than glial heterotopias. The embryology of such lesions is considered, and likely differs from the much more common occipital encephalocele arising from one or both occipital lobes.